文章：

儿童肝脏未分化胚胎性肉瘤的治疗

Treatment of Undifferentiated Embryonal Sarcoma of the Liver in Children

原文发布日期：23 February 2024

DOI: 10.3390/cancers16050897

类型: Article

开放获取: 是

英文摘要：

Undifferentiated embryonal sarcoma of the liver is a rare mesenchymal tumor with a highly malignant potential. It occurs almost exclusively in the pediatric population and typically has a poor outcome. Although previous studies have reported dismal prognoses, recent advances in combined treatment modalities, e.g., surgery and chemotherapy, have given cause for optimism. Even in those diseases not amenable to complete surgical resection or refractory diseases, other treatment modalities, such as liver transplant, have yielded promising results. This paper provides a review of the current treatment modalities for hepatic undifferentiated embryonal sarcoma in children.

摘要翻译： 

肝未分化胚胎性肉瘤是一种罕见的间叶组织肿瘤，具有高度恶性潜能。该疾病几乎仅发生于儿童群体，且通常预后不良。尽管既往研究报道其预后较差，但近年来手术联合化疗等综合治疗模式的进展为改善预后带来了希望。即使对于无法完全手术切除或难治性病例，肝移植等其他治疗方式也展现出令人鼓舞的疗效。本文旨在综述当前儿童肝未分化胚胎性肉瘤的治疗策略。

原文链接：

Treatment of Undifferentiated Embryonal Sarcoma of the Liver in Children